» Medical & Health » Diseases » Q00-Q99. Congenital malformations, deformations and chromosomal » Q80-Q89. Other congenital malformations » Q82. Other congenital malformations of skin
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Excludes: acrodermatitis enteropathica (E83.2)
congenital erythropoietic porphyria (E80.0)
pilonidal cyst or sinus (L05.-)
Sturge-Weber (-Dimitri) syndrome (Q85.8)
Q82.0
Hereditary lymphoedema
Q82.1
Xeroderma pigmentosum
Q82.2
Mastocytosis
Urticaria pigmentosa
Excludes: malignant mastocytosis (C96.2)
Q82.3
Incontinentia pigmenti
Q82.4
Ectodermal dysplasia (anhidrotic)
Excludes: Ellis-van Creveld syndrome (Q77.6)
Q82.5
Congenital non-neoplastic naevus
Birthmark NOS
Naevus:
.flammeus
.portwine
.sanguineous
.strawberry
.vascular NOS
.verrucous
Excludes: cafe au lait spots (L81.3)
lentigo (L81.4)
naevus:
. NOS (D22.-)
. araneus (I78.1)
. melanocytic (D22.-)
. pigmented (D22.-)
. spider (I78.1)
. stellar (I78.1)
Q82.8
Other specified congenital malformations of skin
Abnormal palmar creases
Accessory skin tags
Benign familial pemphigus [Hailey-Hailey]
Cutis laxa (hyperelastica)
Dermatoglyphic anomalies
Inherited keratosis palmaris et plantaris
Keratosis follicularis [Darier-White]
Excludes: Ehlers-Danlos syndrome (Q79.6)
Q82.9
Congenital malformation of skin, unspecified
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