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» E00-E90. Endocrine, nutritional and metabolic diseases
» E70-E90. Metabolic disorders
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E78. Disorders of lipoprotein metabolism and other lipidaemias


Excludes: sphingolipidosis (E75.0-E75.3) E78.0 Pure hypercholesterolaemia Familial hypercholesterolaemia Fredrickson's hyperlipoproteinaemia, type Ⅱa Hyperbetalipoproteinaemia Hyperlipidaemia, group A Low-density-lipoprotein-type [LDL] hyperlipoproteinaemia E78.1 Pure hyperglyceridaemia Endogenous hyperglyceridaemia Fredrickson's hyperlipoproteinaemia, type Ⅳ Hyperlipidaemia, group B Hyperprebetalipoproteinaemia Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinaemia E78.2 Mixed hyperlipidaemia Broad- or floating-betalipoproteinaemia Fredrickson's hyperlipoproteinaemia, type Ⅱb or Ⅲ Hyperbetalipoproteinaemia with prebetalipoproteinaemia Hypercholesterolaemia with endogenous hyperglyceridaemia Hyperlipidaemia, group C Tubero-eruptive xanthoma Xanthoma tuberosum Excludes: cerebrotendinous cholesterosis [van Bogaert-Scherer- Epstein] (E75.5) E78.3 Hyperchylomicronaemia Fredrickson's hyperlipoproteinaemia, type Ⅰ or Ⅴ Hyperlipidaemia, group D Mixed hyperglyceridaemia   E78.4 Other hyperlipidaemia Familial combined hyperlipidaemia E78.5 Hyperlipidaemia, unspecified E78.6 Lipoprotein deficiency Abetalipoproteinaemia High-density lipoprotein deficiency Hypoalphalipoproteinaemia Hypobetalipoproteinaemia(familial) Lecithin cholesterol acyltransferase deficiency Tangier disease E78.8 Other disorders of lipoprotein metabolism E78.9 Disorder of lipoprotein metabolism, unspecified

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