» Medical & Health » Diseases » E00-E90. Endocrine, nutritional and metabolic diseases » E70-E90. Metabolic disorders » E78. Disorders of lipoprotein metabolism and other lipidaemias
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Excludes: sphingolipidosis (E75.0-E75.3)
E78.0
Pure hypercholesterolaemia
Familial hypercholesterolaemia
Fredrickson's hyperlipoproteinaemia, type Ⅱa
Hyperbetalipoproteinaemia
Hyperlipidaemia, group A
Low-density-lipoprotein-type [LDL] hyperlipoproteinaemia
E78.1
Pure hyperglyceridaemia
Endogenous hyperglyceridaemia
Fredrickson's hyperlipoproteinaemia, type Ⅳ
Hyperlipidaemia, group B
Hyperprebetalipoproteinaemia
Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinaemia
E78.2
Mixed hyperlipidaemia
Broad- or floating-betalipoproteinaemia
Fredrickson's hyperlipoproteinaemia, type Ⅱb or Ⅲ
Hyperbetalipoproteinaemia with prebetalipoproteinaemia
Hypercholesterolaemia with endogenous hyperglyceridaemia
Hyperlipidaemia, group C
Tubero-eruptive xanthoma
Xanthoma tuberosum
Excludes: cerebrotendinous cholesterosis [van Bogaert-Scherer- Epstein] (E75.5)
E78.3
Hyperchylomicronaemia
Fredrickson's hyperlipoproteinaemia, type Ⅰ or Ⅴ
Hyperlipidaemia, group D
Mixed hyperglyceridaemia
E78.4
Other hyperlipidaemia
Familial combined hyperlipidaemia
E78.5
Hyperlipidaemia, unspecified
E78.6
Lipoprotein deficiency
Abetalipoproteinaemia
High-density lipoprotein deficiency
Hypoalphalipoproteinaemia
Hypobetalipoproteinaemia(familial)
Lecithin cholesterol acyltransferase deficiency
Tangier disease
E78.8
Other disorders of lipoprotein metabolism
E78.9
Disorder of lipoprotein metabolism, unspecified
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