» Medical & Health » Diseases » E00-E90. Endocrine, nutritional and metabolic diseases » E70-E90. Metabolic disorders » E74. Other disorders of carbohydrate metabolism
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Excludes: increased secretion of glucagon (E16.3)
diabetes mellitus (E10-E14)
hypoglycaemia NOS (E16.2)
mucopolysaccharidosis (E76.0-E76.3)
E74.0
Glycogen storage disease
Cardiac glycogenosis
Disease:
. Andersen
. Cori
. Forbes
. Hers
. McArdle
. Pompe
. Tauri
. von Gierke
Liver phosphorylase deficiency
E74.1
Disorders of fructose metabolism
Essential fructosuria
Fructose-1, 6-diphosphatase deficiency
Hereditary fructose intolerance
E74.2
Disorders of galactose metabolism
Galactokinase deficiency
Galactosaemia
E74.3
Other disorders of intestinal carbohydrate absorption
Glucose-galactose malabsorption
Sucrase deficiency
Excludes: lactose intolerance (E73.-)
E74.4
Disorders of pyruvate metabolism and gluconeogenesis
Deficiency of:
. phosphoenolpyruvate carboxykinase
. pyruvate:
. carboxylase
. dehydrogenase
Excludes: with anaemia (D55.-)
E74.8
Other specified disorders of carbohydrate metabolism
Essential pentosuria
Oxalosis
Oxaluria
Renal glycosuria
E74.9
Disorder of carbohydrate metabolism, unspecified
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